INSUFICIENCIA CARDIACA

Insuf Card 2016;11 (3): 115-121

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Pulmonary arterial hypertension in adult congenital heart disease

Impact and outcome

Data from the GUTI-GUCH Registry

Claudio Gabriel Morós, Marisa Pacheco Otero, Gianina Faliva, María del Carmen Rubio,

Mariana López Daneri, Isabel Torres, Inés Abella, Álvaro Sosa Liprandi,

Liliana Noemí Nicolosi, María Grippo

Adult congenital heart disease (ACHD) is one of the fastest growing subgroups in recent years in cardiology due to early diagnosis and progression of surgical and endovascular treatments. It is estimated that 85-90% of patients with congenital heart disease will reach adulthood. The survival of these patients generates complications and sequelae that result in a higher rate of hospitalizations and new surgeries, among other procedures.

It is estimated that 5-10% of patients with ACHD will develop pulmonary hypertension (PH) in their evolution, currently being the most frequent cause of pulmonary arterial hypertension (PAH) after connective tissue diseases. Its occurrence is related with a worse prognosis for the patient.

The objective of the present study was to analyze the epidemiological characteristics, clinical and pharmacological treatment in patients with PAH and their impact on survival.

Vanesa Parra Henao