INSUFICIENCIA CARDIACA

Insuf Card 2016; 11 (3): 115-121

 

Pulmonary Arterial Hypertension in Adult Congenital heart Disease

Impact and Outcome

Data from the GUTI-GUCH Registry

Claudio Gabriel Morόs, Marisa Pacheco Otero, Gianina Faliya, María del Carmen Rubio, Mariana Lόpez Daneri, Isabel Torres, Inés Abella, Álvarado Sosa Liprandi, Liliana Noemí Nicolosi, María Grippo

 

Introduction

 

                  Adult congenital heart disease (ACHD) is one of cardiology’s fastest growing subgroup in recent years due to early diagnosis and advances in surgical and endovascular treatment. It has been calculated that 85-90% of patients diagnosed with congenital heart disease will reach adulthood. The survival of these patients generates complications and consequences that result in greater hospitalization rates and new surgeries among other procedures.

It is estimated that about 5-10% of patients with ACHD will develop pulmonary hypertension (PH) in its progression, making in the most frequent cause for pulmonary arterial hypertension (PAH), after connective tissue disease. Its emergence is related to a worse prognosis for the patient.

The objective of this study was to analyze the epidemiological characteristics, clinical, and pharmacological treatment of patients with PAH as well as their survival rate.